Budd-Chiari Syndrome and Myeloproliferative Disorder
نویسندگان
چکیده
منابع مشابه
Budd-Chiari syndrome and myeloproliferative disorder.
Budd-Chiari syndrome (BCS) is a rare clinicopathological condition characterized by occlusion of the major hepatic veins with or without membranous obstruction (MOVC)of the inferior vena cava (IVC) at its hepatic portion. Ascites, hepatomegaly and upper abdominal pain constitute the classical triad of symptoms, and the disease usually progresses to congenital liver cirrhosis and portal hyperten...
متن کاملBudd-Chiari syndrome caused by hepatic vein thrombosis in a patient with myeloproliferative disorder.
We report a 24-year-old Japanese female hospitalized with jaundice and ascites. She exhibited hepatosplenomegaly, severe liver dysfunction, and slight polycythemia with an increase in serum levels of beta-thromboglobin and platelet factor 4. Bone marrow was hypercellular with an increase in progenitor cells. The aggregation response of platelets to ADP and to collagen was markedly increased. Ve...
متن کاملBudd-Chiari Syndrome
Budd-Chiari syndrome (BCS) is a rare condition which occurs when there is obstruction of the hepatic veins. It includes any condition in which there is obstruction to venous flow from the small hepatic veins to the inferior vena cava. It should be differentiated from veno-occlusive disease in which the sinusoidal epithelial cells of the hepatic venules are damaged; this mainly occurs after stem...
متن کاملAnticoagulation and Budd-Chiari syndrome.
To the Editor, We read with interest the article by Shukla and Bhatia [1] in a recent issue of the Journal. The authors found that 6 of their patients could not undergo the standard radiological procedures because of technical reasons; reasons for this technical failure were however, not provided. In our experience of adult patients, the TIPSS procedure is usually possible. Of 58 patients who u...
متن کاملBudd-Chiari syndrome.
Budd-Chiari syndrome is the generic term for different forms of hepatic venous outflow obstruction resulting in a clinical picture of portal hypertension and hepatomegaly. Three levels of venous outflow obstruction may be recognized, affecting respectively the small intrahepatic (IVC). Each level of obstruction is related to a different aetiology. Clinical manifestations range from mild symptom...
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ژورنال
عنوان ژورنال: Internal Medicine
سال: 1996
ISSN: 0918-2918,1349-7235
DOI: 10.2169/internalmedicine.35.837